Cystic nephroma is a rare, multicystic, non-hereditary benign lesion that does not contain solid components. The fact that this entity can not be easily distinguished from other cystic tumors of kidney creates difficulties in diagnosis and treatment. We present a 37-year-old male case with incidentally detected two cystic masses in his left kidney. After nephron-sparing nephrectomy, the histopathology of one of the cystic mass of the patient was reported as renal cell cancer and the other as cystic nephroma. Cystic nephroma is a rare tumor of the kidney. Definitive diagnosis can be made histopathologically rather than using physical examination and imaging methods. We reviewed the literature by presenting our case that had 2 cystic lesions in the same kidney, one of which was renal cell cancer and the other was cystic nephroma.

Keywords : cystic nephroma, renal cell cancer, cortical cyst, nephrectomy