Nephroblastoma (Wilms Tumor / WT) is the rare but the most common primary kidney tumor in children. The WT is generally diagnosed between 1 and 5 and the most common diagnosis is the age of 3. Up to 95% of WTs are diagnosed correctly with visualization (ultrasound, computed tomography and magnetic resonance). Histopathologicaly tissue examination is implemented and subtypes are determined. Surgery is one of the key factors in WT treatment. Transperitoneal radical nephrectomy is the standard operation for unilateral WTs. Nephron sparing surgery (partial nephrectomy) is suggested only in selected cases with a single kidney or bilateral WT. Other treatment combination for Wilms tumor involves chemotherapy and radiation treatment. A patient who was diagnosed with Wilms tumor in the right kidney and underwent partial nephrectomy which is rarely implemented or recommended in selected cases is represented in this article.

Keywords : Wilms tumor, child, partial nephrectomy